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#Auditory neuropathy spectrum disorder recommendaions series

There is no cure for auditory neuropathy. Treatment options for auditory neuropathy other tests – to rule out other conditions that may present similar symptoms, such as multiple sclerosis.Generally speaking, a person with auditory neuropathy performs poorly when the test is given with background noise other hearing tests – such as speech recognition.

Typically, a person with auditory neuropathy has some properly functioning hair cells If so, the microphone will pick up the faint sounds made by the hairs as they respond to noise. otoacoustic emissions (OAE) – a tiny microphone is placed inside the ear canal to check whether the cochlear hair cells are working.Typically, a person with auditory neuropathy has little or no response

#Auditory neuropathy spectrum disorder recommendaions series

auditory brainstem response (ABR) – electrodes on the ears and head detect brain wave patterns when the person is exposed to a series of sounds.

This suggests a genetic component.Īuditory neuropathy is diagnosed using a number of tests including:

other affected family members – some children with auditory neuropathy have similarly affected family members.

other disorders – in rare cases, auditory neuropathy is associated with other neurological disorders such as Charcot-Marie-Tooth disorder and Friedrich’s ataxia.

health problems at birth – such as premature birth, jaundice or low birth weight.

particular medications – certain medications that are used to treat obstetric complications are thought to affect the inner ear hair cells in susceptible babies.

health problems in utero – such as reduced oxygen supply to the fetus.

the eighth cranial nerve (the combination of the cochlear and vestibular nerves)Īnyone can be affected, but known risk factors for auditory neuropathy in children include:.

the connections between the hair cells and the cochlear nerve.

The cause of auditory neuropathy isn’t known, but researchers suspect that a number of factors may be responsible, including damage to: When someone has auditory neuropathy, some of the structures within the ear may be working perfectly, but the information from the ear may be distorted on its way to the brain. The electrical impulses are interpreted by the brain and the sound is ‘heard’. The brain stem is located at the base of the skull, and is considered the ‘bridge’ between the brain and the spinal cord.

brain – the impulse is sent by the cochlear nerve along the eighth cranial nerve to the auditory pathways in the brain stem.

Tiny hair-like nerve endings within the cochlea sense the vibration and pass the message – interpreted into electrical impulses – to the cochlear nerve

inner ear – the amplified sound waves are picked up by a little spiral-shaped organ called the cochlea.

The movement is amplified by tiny bones within the middle ear The eardrum moves in response to sound waves.

middle ear – separated from the outer ear by the eardrum.Sounds are funnelled into the middle ear by the outer ear The different structures involved in hearing include: Many of the symptoms of auditory neuropathy can also be caused by more common types of hearing loss. worsened speech perception in noisy environments.normal hearing but with poor speech perception.difficulty understanding spoken words (speech perception).The symptoms of auditory neuropathy vary from one person to the next, and can fluctuate. For example, the hearing of a person diagnosed with auditory neuropathy may improve, deteriorate or remain unchanged, and there is no way to predict the outcome. Symptoms of auditory neuropathy can sometimes vary for example, a person may experience both improvements and deteriorations in their hearing. Hearing and understanding speech may be improved by the use of hearing aids or cochlear implants. In some cases, the affected person can hear, but has difficulty understanding spoken words, particularly in noisy environments. Auditory neuropathy is sometimes referred to as a form of neural or nerve deafness. Both ears are usually affected, and the hearing loss ranges from mild to severe. It is caused by disruption of the nerve impulses travelling from the inner ear to the brain, although what causes this is unknown, and there is no cure. Auditory neuropathy is a rare type of hearing loss.